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Bookmark or Share- Blistering skin conditions - DermNetWhat is a blistering disease? A blistering disease is a condition in which there are fluid-filled skin lesions. Vesicles are small blisters less than 5 mm in diameter. A bulla is a larger blister. Note that the plural of bulla is bullae. Blisters may break or the roof of the blister may become detached forming an erosion.
- Hailey-Hailey disease (benign familial pemphigus) - DermNetBenign familial pemphigus is also known as Hailey–Hailey disease. It is a rare hereditary blistering skin disease first described by the Hailey brothers in 1939. Unrelated to pemphigus vulgaris, Hailey-Hailey disease is not an autoimmune condition and has a differing prognosis.
- Pemphigus vulgaris pathology - DermNetHailey-Hailey disease: Disruption of epithelium adjacent to bullae (intact in pemphigus vulgaris) with sparing of adnexal structures. Immunofluorescence is negative. Pemphigus foliaceus: Acantholysis more superficial within the granular layer. Lacks mucous membrane involvement. Grover disease: There is a pemphigus-like form of this disease ...
- Hailey-Hailey disease pathology - DermNetFamilial benign pemphigus, also called Hailey–Hailey disease, is an acantholytic skin disorder caused by mutations in the ATP2C1 gene, with autosomal-dominant inheritance. The ATP2C1 gene is vital for keratinocyte adhesion and differentiation. Histology of benign familial pemphigus
- Darier disease pathology - DermNetHailey-Hailey disease: the key difference here is the breadth of involvement of the epidermis by the acantholysis. There are more pronounced areas of partially and completely acantholytic cells. There are more pronounced areas of partially and completely acantholytic cells.
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